Fibrose kystique
Description
Veille informationnelle portant sur la fibrose kystique
Sujets couverts
Fibrose kystique
Diagnostic et évaluation
Interventions et traitements
Transplantation
Mode de vie et approches complémentaires
Expériences des patients et des institutions
Sources
PubMed
Fréquence
Mensuelle
Bibliothécaire responsable
Caroline Dion
caroline.dion.chum@ssss.gouv.qc.ca
Général
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Environmental Exposures, Chronic Sinusitis, and Olfaction in People With Cystic Fibrosis
Le 21 octobre 2026
Int Forum Allergy Rhinol. 2026 Oct 18. doi: 10.1002/alr.70204. Online ahead of print. ABSTRACT BACKGROUND: Environmental air pollutants may contribute to chronic rhinosinusitis (CRS), but their…
Diagnostic et évaluation
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Assessment of Cystic Fibrosis Lung Disease Using Electrical Impedance Tomography
Le 21 octobre 2026
Pediatr Pulmonol. 2026 Oct;61(10):e71856. doi: 10.1002/ppul.71856. ABSTRACT INTRODUCTION: Electrical impedance tomography (EIT) is a non-invasive, effort-independent imaging technique for measurement…
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Beyond Tuberculosis: Late Diagnosis of Cystic Fibrosis in an Adolescent with Bronchiectasis and Recurrent Pseudomonas aeruginosa Isolation: A Case Report
Le 21 octobre 2026
Diagnostics (Basel). 2026 Sep 24;16(19):3102. doi: 10.3390/diagnostics16193102. ABSTRACT Background and Clinical Significance: Cystic fibrosis may remain undiagnosed until adolescence, when recurrent…
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MicroRNAs during Echinococcus spp. infection: a comprehensive systematic review and implications for diagnosis and therapy
Le 21 octobre 2026
Parasit Vectors. 2026 Jul 23;19(1):453. doi: 10.1186/s13071-026-07581-0. ABSTRACT BACKGROUND: MicroRNAs (miRNAs) are a subclass of small non-coding RNAs that regulate gene expression and play…
Interventions et traitements
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Pulmonary delivery of ivacaftor via proliposomal dry powder inhalers for cystic fibrosis therapy
Le 21 octobre 2026
J Liposome Res. 2026 Oct 6:1-12. doi: 10.1080/08982104.2026.2738469. Online ahead of print. ABSTRACT Ivacaftor, a CFTR potentiator, is clinically effective in treating cystic fibrosis (CF), but it…
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Treatment adherence and mental health in people with cystic fibrosis and advanced lung disease treated with elexacaftor/tezacaftor/ivacaftor
Le 21 octobre 2026
Pulmonology. 2026 Dec;32(1):2742596. doi: 10.1080/25310429.2026.2742596. Epub 2026 Oct 12. ABSTRACT INTRODUCTION: Advanced lung disease (ALD) is a leading cause of mortality in cystic fibrosis (CF)…
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How cystic fibrosis modulator therapy could transform Pseudomonas aeruginosa epidemiology
Le 21 octobre 2026
Microbiology (Reading). 2026 Oct;172(10). doi: 10.1099/mic.0.001790. ABSTRACT The advent of cystic fibrosis transmembrane conductance regulator modulators has revolutionized cystic fibrosis (CF) care…
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From historical dosing to precision dosing: Modernising tobramycin monitoring in people with cystic fibrosis
Le 21 octobre 2026
Eur J Clin Pharmacol. 2026 Oct 17;82(11):271. doi: 10.1007/s00228-026-04205-5. ABSTRACT BACKGROUND: Historical therapeutic drug monitoring (TDM) strategies for intravenous tobramycin in people with…
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Bacteriophage Therapy in Cystic Fibrosis: Emerging Strategies for Managing Chronic Pseudomonas aeruginosa Infections
Le 21 octobre 2026
Drug Des Devel Ther. 2026 Oct 14;20:612130. doi: 10.2147/DDDT.S612130. eCollection 2026. ABSTRACT Pseudomonas aeruginosa is the leading cause of chronic respiratory infection in people with cystic…
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Olfactory Function in Cystic Fibrosis: Outcome Measures, Olfactory Dysfunction Prevalence and the Impact of Management-A Systematic Review and Meta-Analysis
Le 21 octobre 2026
Int Forum Allergy Rhinol. 2026 Sep 21. doi: 10.1002/alr.70275. Online ahead of print. ABSTRACT BACKGROUND: Olfactory dysfunction (OD) is an increasingly recognized but under-investigated comorbidity…
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Perspectives on inhaled medicines in the CFTR modulator era: A national survey of adults with cystic fibrosis
Le 21 octobre 2026
J Cyst Fibros . 2026 Oct 10:S1569-1993(26)03771-9. doi: 10.1016/j.jcf.2026.10.001. Online ahead of print. ABSTRACT INTRODUCTION: The transformative effects of CFTR modulators (CFTRm) have led people…
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Adverse effects of vanzacaftor-tezacaftor-deutivacaftor in a cystic fibrosis population: A case series
Le 18 septembre 2026
Respir Med Case Rep. 2026 Aug 10;63:102474. doi: 10.1016/j.rmcr.2026.102474. eCollection 2026. ABSTRACT Vanazacaftor-Tezacaftor-Deutivacaftor (VTD) is a novel cystic fibrosis transmembrane receptor …
Transplantation
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Microbiological Dynamics Before and After Lung Transplantation: Clinical Interpretation and Prognostic Implications
Le 21 octobre 2026
Clin Transplant. 2026 Oct;40(10):e70702. doi: 10.1111/ctr.70702. ABSTRACT Respiratory cultures before and after lung transplantation are frequently obtained but often difficult to interpret. A…
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Lung transplant perspectives in the era of elexacaftor/tezacaftor/ivacaftor (ETI): Navigating clinical uncertainty and ETI limbo among people with cystic fibrosis, a qualitative analysis
Le 21 octobre 2026
Heart Lung. 2026 Oct 8;80:102969. doi: 10.1016/j.hrtlng.2026.102969. Online ahead of print. ABSTRACT BACKGROUND: Improved health among people with cystic fibrosis (PwCF) taking highly effective…
Mode de vie et approches complémentaires
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Patient-centred understanding of quality of life, symptoms, health equity in cystic fibrosis (PULSE-CF): study protocol for an observational study
Le 21 octobre 2026
BMJ Open Respir Res. 2026 Sep 25;13(1):e004440. doi: 10.1136/bmjresp-2026-004440. ABSTRACT INTRODUCTION: Cystic fibrosis (CF) is a progressive, life-limiting condition affecting more than 160 000…
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Evaluating Dietary Assessment Methods in Adults with Cystic Fibrosis in the Modulator Era: A Comparison of Food Frequency Questionnaires and Three-Day Food Diaries
Le 21 octobre 2026
Nutrients. 2026 Sep 14;18(18):3002. doi: 10.3390/nu18183002. ABSTRACT Background/Objectives: With advances in treatment, nutritional priorities in Cystic Fibrosis (CF) have shifted towards long-term…
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Natural Products Targeting Airway Inflammation and Mucus Hypersecretion: Molecular Mechanisms and Therapeutic Potential for Respiratory Health
Le 18 septembre 2026
Nutrients. 2026 Aug 8;18(16):2599. doi: 10.3390/nu18162599. ABSTRACT Chronic respiratory diseases, including asthma, chronic obstructive pulmonary disease (COPD), bronchiectasis, cystic fibrosis, and…
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"I know that exercise is very good for me": perception of pediatric patients with cystic fibrosis about physical exercise program
Le 18 septembre 2026
Rev Paul Pediatr. 2026 Aug 24;44:e2025358. doi: 10.1590/1984-0462/2026/44/2025358. eCollection 2026. ABSTRACT OBJECTIVE: To explore and understand the perception of children and adolescents with…
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Feeding practices, behaviours and disorders in infants and children with cystic fibrosis: A scoping review
Le 18 septembre 2026
J Acad Nutr Diet. 2026 Aug 29:156836. doi: 10.1016/j.jand.2026.156836. Online ahead of print. ABSTRACT BACKGROUND: Feeding practices and behaviours in children with cystic fibrosis (cwCF) are thought…
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Moving beyond treatment: pulmonary function, autonomous motivation, and physical activity enjoyment in adults with cystic fibrosis
Le 18 septembre 2026
BMC Pulm Med. 2026 Sep 7;26(1):400. doi: 10.1186/s12890-026-04661-w. ABSTRACT BACKGROUND: Physical activity (PA) and structured exercise are established cornerstones of cystic fibrosis (CF)…
Expériences des patients et des institutions
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"I gained a superpower... is this how normal people feel?": A qualitative exploration of dietary perspectives and experiences amongst adults living with Cystic Fibrosis in the modulator era
Le 21 octobre 2026
J Acad Nutr Diet. 2026 Sep 28:156892. doi: 10.1016/j.jand.2026.156892. Online ahead of print. ABSTRACT BACKGROUND: Cystic Fibrosis (CF) care has been transformed by modulator therapies, extending…
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Assessment of pMDI inhaler technique in children and adolescents with cystic fibrosis
Le 21 octobre 2026
J Pediatr (Rio J). 2026 Sep 24:101624. doi: 10.1016/j.jped.2026.101624. Online ahead of print. ABSTRACT OBJECTIVE: To assess the quality of pressurized metered-dose inhaler (pMDI) technique among…
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Care of the Sexual or Gender Minority Community Living with Cystic Fibrosis: A Survey of United States and Canadian Multidisciplinary Health Care Providers
Le 21 octobre 2026
LGBT Health. 2026 Oct 12:23258292261495120. doi: 10.1177/23258292261495120. Online ahead of print. ABSTRACT PURPOSE: Lesbian, gay, bisexual, transgender, queer, intersex, asexual, or another sexual…
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Comfort discussing financial challenges and accessing resources in cystic fibrosis care among people with cystic fibrosis and their care partners: A cross-sectional survey study
Le 21 octobre 2026
J Cyst Fibros . 2026 Oct 10:S1569-1993(26)03772-0. doi: 10.1016/j.jcf.2026.10.002. Online ahead of print. ABSTRACT BACKGROUND: People with cystic fibrosis (PwCF) face considerable financial burdens…
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Navigating School While Living With Cystic Fibrosis: Barriers and Support Strategies From the Patient and Family Perspective
Le 21 octobre 2026
Pediatr Pulmonol . 2026 Oct;61(10):e71870. doi: 10.1002/ppul.71870. ABSTRACT OBJECTIVE: Managing cystic fibrosis (CF) requires balancing medical treatments with age-appropriate activities and…
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Pregnancy in Patients With Cystic Fibrosis
Le 18 septembre 2026
Obstet Gynecol. 2026 Sep 1;148(3):e191-e192. doi: 10.1097/AOG.0000000000006374. NO ABSTRACT PMID: 42623685 | DOI: 10.1097/AOG.0000000000006374
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Health Care Professionals' Estimation of Home Spirometry Use Among People With Cystic Fibrosis: Cross-Sectional Study
Le 18 septembre 2026
JMIR Form Res. 2026 Aug 26;10:e93545. doi: 10.2196/93545. ABSTRACT BACKGROUND: Home spirometry has been widely adopted in the delivery of cystic fibrosis (CF) care. While existing literature largely…
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CFTR Modulator Therapy and Aerobic Fitness Changes in Aerobic Fitness Following Initiation of CFTR Modulator Therapy: A Systematic Review and Meta-Analysis
Le 18 septembre 2026
Pediatr Pulmonol. 2026 Sep;61(9):e71826. doi: 10.1002/ppul.71826. ABSTRACT INTRODUCTION: Cystic fibrosis transmembrane conductance regulator (CFTR) modulator therapy has led to relevant clinical…
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Mental health safety profile of CFTR modulators in pediatrics and adults: insights from the French pharmacovigilance database and from VigiBase
Le 18 septembre 2026
Ann Am Thorac Soc. 2026 Sep 7:aaoag192. doi: 10.1093/annalsats/aaoag192. Online ahead of print. ABSTRACT RATIONALE: CFTR modulators (CFTRms) have transformed cystic fibrosis care, yet concern exists…
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Impact of an Integrated Health System Specialty Pharmacy on Clinical and Operational Outcomes in Patients with Cystic Fibrosis
Le 18 septembre 2026
Am J Health Syst Pharm. 2026 Sep 9:zxag275. doi: 10.1093/ajhp/zxag275. Online ahead of print. ABSTRACT PURPOSE: Pharmacist inclusion in the cystic fibrosis (CF) multidisciplinary care team is…
